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Home Rare case of desmoid-type fibromatosis of the mandibular region in...

Rare case of desmoid-type fibromatosis of the mandibular region in a child: diagnosis and surgical management

Authors:

  • D. Burlini
    AO Spedali Civili Brescia, Dep. Pediatric Maxillo Facial Surgery, Brescia, Italy
  • G. Conti
    University of Milano- IRCCS
  • E. Bardellini
  • F. Amadori

ABSTRACT


Aim

Desmoid-type fibromatosis is a broad group of rare disorders that originate from musculoaponeurotic structures. They
represent less than 0,1 off all tumors and the annual incidence is 2-4 cases per million, with two peaks between 6 and 15 years
of age and between puberty and age 40. They are rare in the oral and maxillofacial regions. Its pathogenesis is multifactorial. The
treatment is still mainly represented, both in children and adults, by surgical excision. CASE REPORT: A case is reported of a 8-year-
old girl with desmoid fibroma in the mandible who presented at the Department of Pediatric Dentistry with a swelling measuring 4x4 cm
on the lower edge of the right mandible which had appeared a few months earlier and slowly developed. The family dentist had initially
diagnosed it as an odontogenic abscess from the lower right deciduous molars, but the antibiotic therapy was unsuccessful. After x-ray
examination, which showed a large osteolytic lesion, mandibular CT revealed a solid expanding mass. The child was referred to the
Department of Paediatric Maxillofacial Surgery where the whole mass was surgically removed. At the 2-year follow-up no relapse was
noted.

Conclusion

This case stresses the importance, especially for paediatric dentists, of further diagnostic steps if suspect lesions
do not heal after conventional treatment.

PLUMX METRICS

Publication date:

Dec /2013

Keywords:

children, desmoid-type fibromatosis, maxillofacial surgery

Issue:

Vol.14 – n.4/2013

Page:

333 – 334

Publisher:

Ariesdue

Cite:


Harvard: D. Burlini, G. Conti, E. Bardellini, F. Amadori (2013) "Rare case of desmoid-type fibromatosis of the mandibular region in a child: diagnosis and surgical management", European Journal of Paediatric Dentistry, 14(4), pp333-334. doi:
Vancouver: D. Burlini, G. Conti, E. Bardellini, F. Amadori. Rare case of desmoid-type fibromatosis of the mandibular region in a child: diagnosis and surgical management. European Journal of Paediatric Dentistry [Internet]. 2013Dec.1 [cited 2023Mar.21];14(4):333-334. Available from: https://www.ejpd.eu/abstract-pubmed/rare-case-of-desmoid-type-fibromatosis-of-the-mandibular-region-in-a-child-diagnosis-and-surgical-management/
MLA: D. Burlini, G. Conti, E. Bardellini, F. Amadori Rare case of desmoid-type fibromatosis of the mandibular region in a child: diagnosis and surgical management. European Journal of Paediatric Dentistry. 2013;14(4):333-334

Copyright (c) 2021 Ariesdue

Creative Commons License

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

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    European Journal of Paediatric Dentistry © | ISSN (Online): 2035-648X
    Registrazione del Tribunale di Milano n. 285 del 14.04.1998 | ROC 1946 - 26.09.2001
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